Bio Chemistry

Bio Chemistry

Introduction

The world of biochemistry is filled with many disorders, many of which the human may be unaware of. Out of these many disorders, the following paper discusses hereditary fructose intolerance disorder and mitochondrial diseases.

Discussion

Hereditary Fructose Intolerance

Hereditary Fructose Intolerance, a disorder, is a state in which person does not have sufficient proteins in order to breakdown the fructose elements in the body that occurs naturally. The disorder is usually caused because of the absence of enzymes known as Aldolase B. If the human body consumes sugar elements and does not have sufficient fructose to break down sugars, it may result in complex chemical reactions inside the body decreasing the blood sugar and destroying the liver. It is an inherited disease that is passed through generations and families and is mostly found in similar genes transmitted during birth.

Enzymes and breakdown of Fructose

Enzymes are catalytic proteins that speed up chemical reactions occurring inside the body. The body functions remain slow if there are no enzymes in the body. The processes are a part of a cycle and these processes cannot occur if there are no specific enzymes acting as catalysts. One example of this is the function of the breaking down of fructose through an enzymatic function.

Fructose is a sugar found in foods such as sugar and honey. It is a great energy source of the body and provides necessary carbohydrates. Fructose does not provide energy to the body directly; it has to be broken down by enzymes to come up with usable energy.

The initial stage of fructose catabolism is known as fructolysis which begins with the functioning of enzyme known as fructokinase, found in the liver and fructose 1-phosphate is produced. The next stage splits the product into dihydroxyacetone phosphate and glyceraldehyde through Adolase B enzyme. These ...